Angiokeratoma circumscriptum was first described in 1915 by Fabry.1 Angiokeratoma scroti was described by Fordyce2 in 1896. These two entities are compared to the other angiokeratomata in Table 1. For references from the older literature on the angiokeratoma circumscriptum, the reader is referred to the paper of Loria, Derbes and Krafchuk.3 For references on the angiokeratoma scroti, see Robinson and Tasker,4 and Izaki.5
I wish to report the case of a patient with angiokeratoma circumscriptum, angiokeratoma scroti, and "caviar spots of the tongue" (Bean6). The discussion will be directed towards establishing the nature of these vascular lesions.
Report of Case
An 80-year-old white man was admitted to the Portland Veterans Administration Hospital for operation on a hernia. When he was approximately 67, he noticed a red spot near the right ankle. This became larger with time, and developed a "roughness" (hyperkeratosis). Other spots