Dermatofibrosarcoma Protuberans. Presented by Dr. Theodore Cornbleet and Dr. Earl R. Pace.
This Negro, aged 28, presents a tumor situated roughly in the midline above the umbilicus and states that he noted the first nodule in this area twelve years ago. He has no knowledge of preceding trauma. The lesion has progressed slowly and asymptomatically.
There is an irregular hard sharply circumscribed platelike tumor, 8 by 4 cm., apparently originating in the skin but freely movable over the underlying tissues. It presents numerous pea-sized nodular irregularities of the surface with variable pigmentation, two dark reddish, nipple-shaped nodules from 1 to 2 cm. in diameter and one large soft dark red pedunculated globular tumor 3.5 cm. in diameter. The only ulceration or crusting is on the lower part of this tumor, where the belt caused irritation.
The Kahn reaction was negative.
A biopsy specimen from the right nipple-like nodule showed that